Síndrome de Rapunzel con perforación intestinal en gestante

Abstract

Rapunzel syndrome is a rare entity, more so in pregnant women that is complicated by an intestinal perforation. We report the case of a 30-year-old patient, 29 weeks of gestational age, with past medical history of chronic anemia and malnutrition, admitted for an acute abdominal condition and abdominal focus sepsis. Surgical exploration reveals multiple intestinal perforations due to trichobezoar which are approached surgically by performing resection and intestinal anastomosis, keeping the fetus alive. Days later acute fetal distress, septic shock and anastomosis dehiscence are evidenced , and later the patient dies. Given the background, pregnancy status and underlying pathology, the importance of clinical evaluation, auxiliary tests, multidisciplinary management and therapeutic decision for the management of this disease, which in our case has a fatal outcome, is highlighted.